Journal of Indian Society of Pedodontics and Preventive Dentistry
Journal of Indian Society of Pedodontics and Preventive Dentistry
                                                   Official journal of the Indian Society of Pedodontics and Preventive Dentistry                           
Year : 2011  |  Volume : 29  |  Issue : 6  |  Page : 66--69

Dental management of PHACE syndrome under general anesthesia


S Fernandes1, A Kakade2, AM Jetpurwala2, B Patil1, S Jain2, P Kasar2 
1 Department of Anesthesiology, T. N. Medical College and B. Y. L. Nair Charitable Hospital, Mumbai, India
2 Department of Pediatric Dentistry, Nair Hospital Dental College, Mumbai, India

Correspondence Address:
A Kakade
Department of Pediatric Dentistry, Nair Hospital Dental College, Dr. A. L. Nair Road, Mumbai Central, Mumbai - 400 008
India

PHACE syndrome was first described by Dr. Ilonia Frieden and colleagues in 1996. It is an under-recognized rather than a very rare condition among patients with large facial hemangiomas. It is challenging as it has significant neurological, vascular and airway implications. Vascular malformations compromising cerebral blood flow predispose the patient to strokes and seizures. Subglottic hemangiomas, if present, could bleed during intubation. Meticulous neurological monitoring is mandatory in those undergoing repair of the great vessels. We describe the perioperative management of a child with PHACE syndrome subjected to dental treatment under general anesthesia.


How to cite this article:
Fernandes S, Kakade A, Jetpurwala A M, Patil B, Jain S, Kasar P. Dental management of PHACE syndrome under general anesthesia.J Indian Soc Pedod Prev Dent 2011;29:66-69


How to cite this URL:
Fernandes S, Kakade A, Jetpurwala A M, Patil B, Jain S, Kasar P. Dental management of PHACE syndrome under general anesthesia. J Indian Soc Pedod Prev Dent [serial online] 2011 [cited 2022 May 24 ];29:66-69
Available from: https://www.jisppd.com/article.asp?issn=0970-4388;year=2011;volume=29;issue=6;spage=66;epage=69;aulast=Fernandes;type=0