CASE REPORT |
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Year : 2019 | Volume
: 37
| Issue : 3 | Page : 303-307 |
Cu-sil dentures: A novel approach of Papillon–Lefèvre syndrome management
Shreya Tyagi1, Abi M Thomas1, Vinod Balla2, Ruchika Kundra1
1 Department of Pedodontics and Preventive Dentistry, Christian Dental College, Ludhiana, Punjab, India 2 Department of Dentistry, Rajiv Gandhi Institute of Medical Sciences, Adilabad, Telangana, India
Correspondence Address:
Dr. Shreya Tyagi Department of Pedodontics and Preventive Dentistry, Christian Dental College, Brown Road, Ludhiana - 141 008, Punjab India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/JISPPD.JISPPD_256_18
Papillon–Lefèvre syndrome (PLS) is a rare genetic disorder characterized by palmoplantar keratosis and premature loss of primary and permanent dentition. Its onset can be as early as 1–4 years of age. The genetic disorder is mutation in the cathepsin C gene. Hereby, we discuss the fabrication of Cu-sil dentures for the prosthetic rehabilitation of a 14-year-old girl with PLS. The case report describes the procedure and associated relevant information regarding the management protocols.
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